PPT-Hypotonia , neuromuscular disorders

Dr Redab AlGhawanmeh Objectives Floppy infant SMAs Neuropathies Muscular dystrophies Congenital myopathies Myotonic dystrophy Myasthenic syndromes Malignant hyperthermia Floppy infant. Overview of the Neuromuscular System . Nervous . system and muscles are working together to . allow movement . In order t. o . move a part. of . your . body, . a message is sent to particular nerve cells which are called upper motor neurons. . Physiology of Muscle Fibers. Action Potentials: The Role of Motor Neurons. Motor neurons . produce motion by interacting . with skeletal muscle.. Electric signals called . action potentials. are sent along nerve cells to muscle fibers.. (PNF). Objectives:. Describe a brief history of PNF.. Define PNF.. List the purposes of PNF.. Be able to apply PNF when working with patients.. Brief History of PNF . ¹. Mid-1940’s: Neurophysiologist Dr. Herman Kabat developed PNF to rehabilitate the muscles of polio patients. MD. Chief Resident, Division of Child Neurology. Department of Pediatrics and Neurology. University of Louisville . Evaluation . of the Hypotonic Infant. Objectives. Factors . related to the production of muscle tone in infants and . PALSY. Definition & Epidemiology. A group of . non progressive . disorders of movement and posture caused by . abnormal development . or . damage . to parts of brain that control muscle movements.. Overview of the Neuromuscular System . Nervous . system and muscles are working together to . allow movement . In order t. o . move a part. of . your . body, . a message is sent to particular nerve cells which are called upper motor neurons. . Nancy Bass, MD. Pediatric Neurology. University Hospitals of Cleveland. Rainbow Babies and Children’s Hospital. I . am a paid . consultant of . Biogen. . and . all material contained within complies with applicable FDA regulations.. Neuromuscular junction. Neuromuscular junction :. the synapse between motor neuron and muscle . fibre. Motor neurons :. are the nerves that innervate (power) muscle . fibres. . Motor unit : . single motor neuron and the muscle . Chris Heine, MD. Medical University of South Carolina. Updated 4/2019. Disclosures. No relevant financial relationships. Learning Objectives. Describe the different classes of neuromuscular disorders. (NMBAs). A self-directed learning module for nurses. April, 2017. Learning Objectives. By successful completion of this self-directed learning (SDL) module and achieving a passing grade of 90% on the post-test, learners will have demonstrated:. Neuromuscular blockade in Critical Care. Aim. . To provide guidance on the administration and monitoring of neuromuscular blockade in Critical Care. Scope. All adult patients in intensive care receiving continuous neuromuscular blockade. A. Definitions Hypotonia can be defined as abnormally low muscle tone, or reduced resistance to passive, relatively rapid movement. The imprecision of the definition reflects the lack of psychometr BY – DR NILANJANA GHOSH. Outlines. Definitions and basic physiology. Differences between central and peripheral causes of hypotonia.. Evaluation of hypotonia in infants.. Management options. Relevant terminologies and definitions. October 2019. Michelle Coady. Neuromuscular Transmission . Skeletal muscle fibers are innervated by large, myelinated nerves . Nerve fibers branch out to stimulate several hundred skeletal muscle fibers.