PPT-Hemophagocytic L ympho

H istiocytosis BY Alireza Shafiei Allergist and Clinical Immunologist Assistant Professor of Tehran University of Medical Sciences Bahrami Hospital Introduction In practice distinction between primary and secondary HLH is not essential for the initial diagnosis and management. Juvenile Xanthogranuloma. Sharon Wu, MD. Dita Gratzinger, MD, PhD. Stanford University. Clinical History. The patient is a 5 month old infant presenting with fever, pancytopenia and splenomegaly of unclear etiology, and two dermal-based translucent papules on the chest and thigh. A skin biopsy was . By: Michelina Kauffman, MD PGY-3. December 4, 2015. Disclosures. Neither Dr. Pirich nor I have any financial disclosures. . Objectives. Untangle the differences between primary HLH, secondary HLH. , and MAS. . Introduction. syndrome of pathologic immune activation characterized by clinical signs and symptoms of extreme inflammation. . It was first recognized as a familial immune . dysregulatory. disorder of childhood, called familial . Syndromes. Samin. . Alavi. Pediatric hematologist oncologist. PCHD-RC, . Shahid. . Beheshti. University of Medical Sciences. Tehran/Iran. Kish- Nov 2018. Diagnosis of HLH. Diagnostic criteria for HLH were proposed by the Histiocyte Society in 1991. 4322 Key Words:Juvenile rheumatoid arthritis (JRA), Juvenile idiopathic arthritis (JIA), Hemophagocytic lymphohistiocytosis (HLH), Regulatory immunological processes.IntroductionJuvenile rheumatoid ar 119 DAHL BLMLER / MEDICAL SCIENCES Olgu Sunumu / Case Report Başvuru tarihi: 12.08.2009 • Kabul tarihi: 11. 05.2010 İletişim Yrd. Doç. Dr. Talia İleri Ankara Ünivers 355 Hemophagocytic lymphohistiocytosis (HLH) represents a severe hyperinflammatory condition with cardinal symptoms 356 Hemophagocytic lymphohistiocytosis (HLH) is a severe life-threatening disease p