PPT-Hemophagocytic Lymphohistiocytosis

By Michelina Kauffman MD PGY3 December 4 2015 Disclosures Neither Dr Pirich nor I have any financial disclosures Objectives Untangle the differences between primary HLH secondary HLH and MAS . Juvenile Xanthogranuloma. Sharon Wu, MD. Dita Gratzinger, MD, PhD. Stanford University. Clinical History. The patient is a 5 month old infant presenting with fever, pancytopenia and splenomegaly of unclear etiology, and two dermal-based translucent papules on the chest and thigh. A skin biopsy was . . DR. KUNAL OSTWAL. JR II. DEPARTMENT OF MEDICINE. CHIEF COMPLAINTS. 22 year/M, resident of Pune, came with c/c of :. . - . Fever : 2 days. . H. istiocytosis. BY: . Alireza. . Shafiei. Allergist and Clinical Immunologist. Assistant Professor of Tehran University of Medical Sciences. Bahrami. Hospital . Introduction:. In . practice, distinction between primary and secondary HLH is not essential for the initial diagnosis and management. Introduction. syndrome of pathologic immune activation characterized by clinical signs and symptoms of extreme inflammation. . It was first recognized as a familial immune . dysregulatory. disorder of childhood, called familial . Syndromes. Samin. . Alavi. Pediatric hematologist oncologist. PCHD-RC, . Shahid. . Beheshti. University of Medical Sciences. Tehran/Iran. Kish- Nov 2018. Diagnosis of HLH. Diagnostic criteria for HLH were proposed by the Histiocyte Society in 1991. 4322 Key Words:Juvenile rheumatoid arthritis (JRA), Juvenile idiopathic arthritis (JIA), Hemophagocytic lymphohistiocytosis (HLH), Regulatory immunological processes.IntroductionJuvenile rheumatoid ar 119 DAHL BLMLER / MEDICAL SCIENCES Olgu Sunumu / Case Report Başvuru tarihi: 12.08.2009 • Kabul tarihi: 11. 05.2010 İletişim Yrd. Doç. Dr. Talia İleri Ankara Ünivers 355 Hemophagocytic lymphohistiocytosis (HLH) represents a severe hyperinflammatory condition with cardinal symptoms 356 Hemophagocytic lymphohistiocytosis (HLH) is a severe life-threatening disease p