PPT-Severe Combined Immunodeficiency

Introduction Benjamin L Wright MD Disclosures I have no relevant financial relationships with the manufacturers of any commercial products andor providers of commercial services discussed in this CME activity . . Izabela. . Fulone. Silvio Barberato Filho. Luciane Cruz Lopes. . THIRD . INTERNACIONAL CONFERENCE . FOR IMPROVING USE . OF . MEDICINES. . Martin Liška. Immunodeficiency. = a disorder of immune system which manifests by impaired ability to carry out basic immunological functions, primarily defence against infection or immunological surveillance. . One infection. too many!. Dr. Ahmad AlKhabaz. , MBBS, FRCPC. Head of Pediatric Allergy & Clinical Immunology . U. nit. Chair of the allergy & immunology exam committee (KIMS). Tutor for the pediatric residency program (KIMS). Prescott Atkinson, MD PhD. Professor and Director. Division of Pediatric Allergy, Asthma & Immunology. University of Alabama at Birmingham. Overview of the Primary Immunodeficiencies:. “Pure” T Cell Disorders. Iga. deficiency - description. Description:. Serum IgA <5 mg/. dL. Normal serum IgG and IgM. Patients >1 year . Genetics:. Autosomal Dominant. Abnormalities on Chromosome 18. Associated with HLA-A1, HLA-A2, B8, and Dw3 . Mutua C, . Karimi. . D, . Irungu. . A, . Patil. . R, . Ngwatu. . P, . Manguyu. W . Kiptum. D. Gertrude’s Children Hospital Nairobi, Kenya. Outline . Background. Methods. Case presentation. BY. DR. JAHNABI. MODERATOR. DR. BHASKAR GUPTA, PROF and HOD. DEPT OF DERMATOLOGY. 1. Introduction. HIV is a . lymphotropic. human retrovirus.. Acquired . - sexually, . - from blood or blood products, or . For MBBS (29.09.2017). By: . Dr. . . Puneet Kumar Gupta. Assistant Professor, M. icrobiology. ,. Introduction. . Immunodeficiency . diseases. Defence . mechanisms of . body are impaired→ repeated . Severe Combined Immunodeficiency (SCID). What is SCID?. Severe . Combined . Immunodeficiency, otherwise known as SCID.. SCID is a group of very rare-and potentially fatal-inherited disorders related to the immune system. . Sohag Medical Journal Faculty of Medicine 158 Mastoid abscess as a presenting c omplaint of Kostmann syndrome in childhood. Ramadan sa i d. Ahmed Ismail. Khaled Ga 1 X-linked severe combined immunodeficiency Description SCIDSCID immune system that occurs almost exclusively in males. Children with X-linked SCID are prone to recurrent and persistent infections be Patients with primary immunodeficiency diseasesmost often are recognized because of their increased(Table 2). In fact, non-infectious manifestations, suchodeficiency. Other immunodeficiency diseases m Hypersensitivities. Hypersensitivity. Any immune response against a foreign antigen exaggerated beyond the norm. Four types. Type I (immediate). Type II (cytotoxic). Type III (immune complex–mediated). Immunodeficiency. = a disorder of immune system which manifests by impaired ability to carry out basic immunological functions, primarily defence against infection or immunological surveillance. Immunodeficies.