PPT-Thalassaemia syndromes Treatment

1 Regular blood transfusions are needed to maintainthe haemoglobin over 10 g dL at all times This usually requires 23 units every 46 weeks Fresh blood filtered to remove white . Objectifs pédagogiques. Quelle est l’anatomo-physiologie de la moelle épinière?. Quelles sont les manifestations cliniques d’une atteinte médullaire?. Comment reconnaitre un syndrome médullaire?. PRESENTED BY:. DR. HITESH GOUR. J.R. PULMONARY MEDICINE. DEFINATION. Paraneoplastic. syndromes refer to the disorders that accompany benign or malignant tumors but are not directly related to mass effects or invasion by the primary tumor or its metastases.. Anaemia. . ?. Anaemia . is defined as reduction in circulating.  . haemoglobin mass below. . the. critical. . level.. The normal . haemoglobin . (Hb) . is . 12-14. . gm%.. . WHO has . accepted . Thalassemia. Beta-thalassaemia is a global disease - most prevalent in South Asia, the Far East, the Middle East, and Mediterranean countries. . Distribution is attributed largely to natural selection of heterozygote carriers because of protection against falciparum malaria. . MD; FRCP (London); . FRCPEdin. ; . FRCSEdin. T. halassemia. Hemoglobin molecule. : is the iron-containing oxygen-transport . metalloprotein. in the red blood cells of all vertebrates.. The normal . haemoglobin. Kakavoulis. . Nikolaos. Patras Ioannis. What is . Thalassaemia. ?. . Thalassaemia. is a group of inherited disorders of hemoglobin synthesis characterized by . reduced . or . absen. ce. . of one . مؤيد . علو. ش. Lec. . 2. Thalassaemias. Objectives:. 1-Define thalassemia and its main types(. β. and . α. ). 2- Know the . genetic . lesions of each of . β . and . α. thalassemia. 3-Know the difference between thalassemia minor and major.. T. halassaemia. , . Diagnosis . & . Management. Dr . Md. . Saqif. . Shahriar. MBBS ,MD(Cardiology). Interventional . cardiologist,NICVD,Dhaka. .. The cardiovascular complications . of . thalassaemia. MB;BS(Ilorin), FWACP(. Paed. ). Outline. Intro /def. Normal haemoglobin structure / function. Classification of haemoglobinopathies . Structural Hb Variants. Thalassaemias. Epidemiology. Clinical features. 1 1 DOI: 10.7860/JCDR/2019/39865.12646 Dentistry Section Radiological Features of Thalassaemia-An Update Review Article Original Article Miscellaneous Postgraduate Education Letter to Editor Short Co مؤيد علوش. Introduction. THE HAEMOGLOBIN MOLECULE. Human . haemoglobin. is formed from two pairs of . globin chains . each with a . haem. . group attached.. Seven . different globin . chains are . Publications Launch Webinar. Thursday 28. th. January 2021. Welcome to NHS Sickle Cell and Thalassaemia Screening Programme’s Live Webinar. Thursday 28. th. January 2021. Chair: Professor Dame Elizabeth N . . Assist. Prof. . Dr.Maysem. . Mouayad. . Alwash. . Note:. The . thalassaemias. are classified into . α. -, . β. -, . δβ. -, . γδβ. -, . δ. -, . γ. - and . εγδβ. -thalassaemias, according to the type of globin chain(s). of . haemoglobin. Ass. . Prof. . . Abeer. . Anwer. Ahmed. Normal adult blood contains three types of . haemoglobin. . Hb. . A . . Hb. . F . . Hb. . A2. Structure .