PPT-Newly diagnosed hemophilia in a 4-year-old with compartment syndrome: A Case Report

Chelsea Marion MD 14 Oluwaseun Odewole MD MPH 24 Sheila Goel MD 34 1 Dept of Pediatrics Morehouse School of Medicine Atlanta GA 2 Dept of Family Medicine Morehouse School of Medicine Atlanta GA . Nairobi, Kenya. June 24, 2013. Objectives. Identify historical approaches used to treat hemophilia. Describe treatment products currently available for use in hemophilia. Distinguish classes of factor concentrates. (. H. aemophilia). By: Morgan Dirienzo. The Royal Disease. Alternate Names and Symptoms. Some alternate names for Hemophilia would be Haemorrhaphilia, or Von Willebrand disease. . The Symptoms for Hemophilia are…. Sathish Rajasekaran, MD, Clinical Assistant Professor, Division of PM&R, University of Alberta. None . Disclosures. Introduction. Anatomy. Pathophysiology. History and Physical Exam. Diagnostic Evaluation. By: Nam-Y7. Hemophilia was first recognized by the Jews, but not officially named even in the ancient times. . In the 2. nd. century AD, the Talmud, a Jewish collection of Rabbinical writings said that the boys did not have to be circumcised if two brothers died of the disease. In 1800s, it became known as the Royal Disease because many people of royal families died or got the disease. Queen Victoria got Hemophilia but she survived. Alexei, the heir apparent to the Russian royal family, suffered from Hemophilia. In 1950s, the first treatment to hemophilia appeared. It was in a type called “fresh frozen plasma”. Nowadays, we are marching towards a cure but there are two treatments. One is called “gene therapy” and the other is called “Recombinant therapy”. A treatment for hemophilia is replacing old blood clots with new ones.. Intracompartmental. Pressure Testing. Dr Leesa Huguenin. MP Sports Physicians. www.mpsportsphysicians.com.au. RECS. 95 % lower leg. 45% anterior compartment. Lateral, deep posterior and superficial posterior. The Definition of Compartment Syndrome. Compartment syndrome is an acute medical condition when blood vessels and nerves are compressed causing tissue death and nerve damage.. The “compartment” is the thick layers of fascia that surround muscle groups. This connective tissue does not stretch. With any bleeding or swelling of the muscle inside the compartment, this will cause pressure to increase dramatically. . Professor, Dept. of Orthopedic Surgery, . Univ. of . Minnesota. Chief, Department of Orthopaedic Surgery . Hennepin County Medical . Center. April 2016. Disclosure Information. Andrew H. Schmidt, M.D.. June. , . 2013. Roger L. Lundblad, Ph.D.. Consultant in Biotechnology. Chapel Hill, North Carolina. http://www.lundbladbiotech.com. And Adjunct Professor, Department of Pathology,. University of North Carolina, Chapel Hill, North Carolina. Sex-linked inheritance; almost all patients male. Female carriers may have mild symptoms. Most bleeding into joints, muscles; mucosal and CNS bleeding uncommon. Severity inversely proportional to factor level. Chi-Wei Lin, I-Ting Liu, Ru-Yi Huang, Wei-. Chieh. Hung, Ching-Jung Ho. E-Da Hospital/I-. Shou. University, Taiwan Health Evaluation and Promotion Association. Background. Diabetes is one of the important chronic disease in modern society, and the occurrence and prognosis of this disease is considered to be correlated with patients’ health belief and behavior. . A new ambition of the World Federation of Hemophilia. WFH Guidelines for the Management of Hemophilia. All recommendations are consensus based.. Srivastava A et al. Haemophilia. 2020;26(Suppl 6):1–158. . Hemophilia A. Also known as Factor VIII Deficiency is the most common type of hemophilia. It is a disorder of your blood-clotting system. Clotting is the process which your blood changes from a liquid to a solid state. Veena Choubey, Rena Malik, and Luis Carlos Zapata Genetics Hemophilia is an X-linked recessive disorder that exists in two forms, hemophilia A and hemophilia B. Hemophilia A is characterized specif Acute Joint Dislocation. Saleh. . WaslAllah. . Alharbi. Professor. KSU. Objectives. Compartment Syndrome (CS). To explain the pathophysiology of CS.. To identify patients at risk.. To be able to diagnose and manage CS..